A 75-Year-Old Natural Survivor with Uncorrected Tetralogy of Fallot Presenting with Hypoxic Spell
- 주제(키워드) Tetralogy of Fallot , Hypoxia , Adult
- 발행기관 Ewha Womans University School of Medicine
- 발행년도 2017
- 원문페이지 5 p.
- 총서유형 Journal
- URI http://www.dcollection.net/handler/ewha/000000142244
- 본문언어 영어
- 저작권 이화여자대학교 논문은 저작권에 의해 보호받습니다.
초록/요약
Tetralogy of Fallot (TOF) is the most common cyanotic congenital heart disease. Only a few patients reach adulthood without surgical correction. Unrepaired TOF patients with mild to moderate right ventricular outflow tract (RVOT) obstruction may be clinically silent until adulthood. TOF with hypoxic spells present as periods of profound cyanosis that occur because of almost total RVOT obstruction. So, hypoxic spell typically occurs in a crying infant but is rare in an adult. In this report, we presented a case of a 75-year-old patient with uncorrected TOF presenting with hypoxic spell, consequent pulmonary hypertension and chronic heart failure. This is the oldest case of natural survivor with uncorrected TOF in Korea and the oldest patient presenting hypoxic spell worldwide. (Ewha Med J 2017;40(2):94-98)
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